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84 Inui K, Yutaka T, Okada S, Yabuuchi H. Wenger DA, Desnik RJ Hexosaminidase A activity in skin fibroblasts from various types of GM2 gangliosidosis using a fluorogenic sulphated substrate. J Inher Metab Dis 8 149-150 1985
85 Inui K, Kao FT, Fujibayashi S, Jones C, Morse HG, Law ML, Wenger DA. The gene coding for a sphingolipid activator protein, SAP-1, is on human chromosome 10. Hum Genet 69 197-200 1985
86 Charrow J, Inui K, Wenger DA Late onset GM2 gangliosidosis: an ƒ¿-locus genetic compound with near normal hexosaminidase activity. Clin Genet 27 78-84 1985
87 Inui K, Wenger DA, Usefulness of 4-methyl-
umbelliferyl-6-sulfo-2-acetamido-2-deoxy-ƒÀ-D-glucopyranoside for the diagnosis of GM2 gangliosidosis in leukocytes.
Clin Genet 26 318-321 1984
88 Fujibayashi S, Inui K, Wenger DA. Activator protein-deficient metachromatic leukodystrophy: diagnosis in leukocytes using immunologic methods. J Pediatr 104 739-742 1984
89 Inui K, Wenger DA Biochemical, immunological, and structual studies on a sphingolipid activator protein (SAP-1). Arch Biochem Biophys 233 556-564 1984
90 Yamono T, Shimada M, Okada S, Yutaka T, Kato T, Inui K,@Yabuuchi H, Kanzaki S, Kanda S. Ultrastructual study on nervous sytem of fetus with GM1-gangliosidosis type 1. Acta Neuropathol 61 15-20 1983
91 Inui K, Grebner EE, Jackson LG, Wenger DA Juvenile GM2 gangliosidosis (‚`M B variant): Inability to activate hexosaminidase A by activator protein. Am J Hum Genet 35 551-564 1983
92 Inui K, Wenger DA. Concentrations of an activator protein for sphingolipid@hydrolysis in liver and brain samples from patients with lysosomal storage disease. J Clin Invest 72 1622-1628 1983
93 Inui K, Emmett M, Wenger DA Immunological evidence for deficiency in an activator protein for sulfatide@sulfatase in a variant form of metachromatic leukodystrophy. Proc Natl Acad Sci USA 80 3074-3077 1983
94 Inui K, Wenger DA. Properties of a protein activator of glycosphingolipid hydrolysis isolated from the liver of a patient with GM1 gangliosidosis, type 1. Biochem Biophys Res Commun 105 745-751 1982
95 Yabuuchi H, Okada S, Yutaka T, Kato T, Inui K Complementation studies on mucolipidosis. Asian Med J 25 501-511 1982
96 Kato T, Okada S, Oshima T, Inui K, Yutaka T, Yabuuchi H. Normalization of intracellular lysosomal hydrolase in I-cell disease fibroblasts with sucrose loading. ‚iBiol Chem 257 7814-7819 1982
97 Yutaka T, Okada S, Kato T, Inui K, Yabuuchi H Galactose-6-sulfate sulfatase activity in Morquio syndrome. Clin Chim Acta 122 169-180 1982
98 Inui K, Okada S, Yutaka T, Kato T, Midorikawa M, Yabuuchi H. Deficiency of phosphotransferase activity of glucose-6-phosphatase in liver specimens of glycogenosis 1a patients. Acta Paediatrica Japonica 24 478-481 1982
99 Yutaka T, Okada S, Kato T, Inui K, Yabuuchi H. Properties of sulfatases in cultured skin fibroblasts of multiple sulfatase deficient patients. Clin Genet 20 296-303 1981
100 Okada S, Yutaka T, Kato T, Inui K, Yabuuchi H, Nishigaki M, Yamashita K, Chiyo H, Furuyama J, Okada Y Mucolipidosis with ƒÀ-galactosidase deficiency: a type of sialidosis. Acta Paediatrica Japonica 23 87-92 1981
101 Kato T, Okada S, Oshima T, Inui K, Yutaka T, Yabuuchi H. Lysosomal hydolase induction in cultured human fibroblasts:@the effect of sucrose. Biochem Int 3 551-556 1981
102 Kato T, Inui K, Yutaka T, Okada S, Yabuuchi H, Chiyo H, Furuyama J Histochemical demonstration of acid beta-D-galactosidase activity in cultured human skin fibroblasts and its application to single cell analysis. Acta@Histochem Cytochem 14 343-349 1981
103 Yutaka T, Kato T, Inui K, Okada S, Yabuuchi H Prenatal diagnosis of Hunter syndrome. Brain & Dev 3 148 1981
104 –÷“à@•SŽ¡A‰ª“c@L‘¾˜YA–L@“OA‰Á“¡@”ºeAŠ£@KŽ¡ ƒ€ƒRƒŠƒsƒh[ƒVƒX‚Ì•aˆö‚ÉŠÖ‚·‚錤‹† “ú–{ˆãŽt‰ïŽGŽ 86 880-886 1981
105 Kodama H, Okada S, Inui K, Yutaka T, Yabuuchi H. Studies on@ƒ¿-ketoglutaric aciduria in type 1 glycogenosis. Tohoku J Exp Med 131 347-353 1980
106 Ha K, Ikeda T, Okada S, Inui K, Tagawa T,. Takada K,@Uchimura N, Kakudo K, Okada A, Yabuuchi H. Hypoglycemia in a child with hepatoblastoma. Medical and Pediatric Oncology 8 335-341 1980
107 Kato T, Okada S, Yutaka T,@Inui K, Yabuuchi H, Chiyo H, Furuyama J, Okada Y Beta-galactosidase defficient-type mucolipidosis: A complementation study of neuraminidase in somatic cell hybrids. Biochem Biophys Res Commun 91 114-117 1979
108 Okada S, Seino Y, Kodama H, Yutaka T, Inui K, Ishida M, Yabuuchi H, Seino Y Insulin and glucagon secretion in hepatic glycogenosis. Acta Paediatr Scand 68 735-738 1979
109 ‘½˜a@º—YAŠ£@KŽ¡AŒÃŒ˜@—S•FA_”ö@Žç–[AŒšÎ@•ÛŽqA–÷“à@•SŽ¡ “ûŽ™‰º—ŸÇ‚É‚¨‚¯‚é“û“œ•ª‰ðy‘f»Ü‚ÌŽg—pŒoŒ± f—ÂƐV–ò 15 1239-1244 1978